Case of the Month: February, 2012, Page 3

Explanation: 

• MelanoticNeuroectodermal Tumor of Infancy.  This is only tumor listed above that increased urinary VMA would be expected.

Question: Regarding melanoticneuroectodermal tumor of infancy,  which of the following is false?

1. Usually arises in infants during first year of life
2. Locally aggressive with frequent distal metastasis
3. Most common location is the maxilla
4. Urine VMA may be elevated